Rare Presentation of Tetralogy of Fallot with Pulmonary Atresia in New Born-A Case Report
Author(s): Prithvi Raj, Ravanagomagan* and Jagadeeswari
Abstract
Tetralogy of Fallot with Pulmonary valve Atresia and Major Aortopulmonary Collateral Arteries (TOF/PA/MAPCAs) is the most extreme variant of TOF. Presentation is relatively rare, with a reported incidence of 0.7 per 10,000 live births. Without flow through PDA, major Aortopulmonary collateral arteries play a major role in maintaining pulmonary blood flow. The management is based on the anatomy of MAPCAs and the nature of PDA. The goal of surgical management is to construct completely separate in series pulmonary and systemic circulations. The Procedure is done by unifocalization, which involves detachment of collateral vessels from their aortic origins and anastomosis to the central pulmonary arteries, followed by reconstruction of RVOT using an allograft valved conduit from the RV that results in ante grade pulmonary blood flow, followed by closure of VSD. Here, we report a case of a Term, boy baby, born to nonconsanguineous parents by caesarean section with birth weight of 2.508 kg. The baby cried immediately after birth with APGAR scores 8 at 1’ and 9 at 5 minutes and did not require resuscitation with subsequent details as follows.